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KMID : 0191120070220040728
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Journal of Korean Medical Science
2007 Volume.22 No. 4 p.728 ~ p.730
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Recurrent Massive Subcutaneous Hemorrhage in Neurofibromatosis Type 1: A Case Report
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Baek Sung-Hoon
Kim Ji-Hye
Kim Jun-Sig
Han Seung-Baik
Cho Jung-Soo
Yoon Yong-Han
Kim Lucia
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Abstract
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Neurofibromatosis type 1 (NF-1) is an autosomal dominant disorder that has three major features: multiple neural tumors, cafe-au-lait spots, and pigmented iris hamartomas (Lisch nodules). The purpose of this case report is to advise physicians of the danger associated with the progression of fast-onset massive hemorrhage to hemodynamic instability, which mandates rapid treatment to prevent the development of a life-threatening condition. A 64-yr-old woman with NF-1 was admitted to the Emergency Department (ED) because of a rapidly growing, 10x5x3 cm-sized mass on the left back area. She had previously undergone surgery for a large subcutaneous hematoma, which had developed on her right back area 30 yr before. She became hemodynamically unstable with hypotension during the next 3 hr after admission to ED. Resuscitation and blood transfusion were done, and the hematoma was surgically removed. The mass presented as a subcutaneous, massive hematoma with pathologic findings of neurofibroma. We report a case of NF-1 that presented as recurrent, massive, subcutaneous hemorrhage on the back region combined with hypovolemic shock.
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KEYWORD
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Neurofibromatosis, Subcutaneous, Hemorrhage
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